Q23.1 Congenital insufficiency of aortic valveBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Defines the logic of DRG(s) 306-307 in MDC 05.
746.4 Congenital insufficiency of aortic valveI35 Nonrheumatic aortic valve disorders ("aortic valve disorder specified as congenital (Q23.0, Q23.1)")I08 Multiple valve diseases ("multiple valve disease specified as nonrheumatic (I34.-, I35.-, I36.-, I37.-, I38.-, Q22.-, Q23.-, Q24.8-)")I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")Q23 Congenital malformations of aortic and mitral valvesQ23.0 Congenital stenosis of aortic valveQ23.1 Congenital insufficiency of aortic valve (this code)Q23.2 Congenital mitral stenosisQ23.3 Congenital mitral insufficiencyQ23.4 Hypoplastic left heart syndromeQ23.8 Other congenital malformations of aortic and mitral valvesQ23.81 Bicuspid aortic valve