Q23.81 Bicuspid aortic valveBillable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.
Defines the logic of DRG(s) 306-307 in MDC 05.
I35 Nonrheumatic aortic valve disorders (", if applicable, bicuspid aortic valve (Q23.81)")I08 Multiple valve diseases ("multiple valve disease specified as nonrheumatic (I34.-, I35.-, I36.-, I37.-, I38.-, Q22.-, Q23.-, Q24.8-)")I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")Q23.1 Congenital insufficiency of aortic valveQ23.2 Congenital mitral stenosisQ23.3 Congenital mitral insufficiencyQ23.4 Hypoplastic left heart syndromeQ23.8 Other congenital malformations of aortic and mitral valvesQ23.81 Bicuspid aortic valve (this code)Q23.82 Congenital mitral valve cleft leafletQ23.88 Other congenital malformations of aortic and mitral valvesQ23.9 Congenital malformation of aortic and mitral valves, unspecified