Q23.2 Congenital mitral stenosisBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Defines the logic of DRG(s) 306-307 in MDC 05.
746.5 Congenital mitral stenosisI34 Nonrheumatic mitral valve disorders ("mitral valve disorder specified as congenital (Q23.2, Q23.9)")I08 Multiple valve diseases ("multiple valve disease specified as nonrheumatic (I34.-, I35.-, I36.-, I37.-, I38.-, Q22.-, Q23.-, Q24.8-)")I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")Q23 Congenital malformations of aortic and mitral valvesQ23.0 Congenital stenosis of aortic valveQ23.1 Congenital insufficiency of aortic valveQ23.2 Congenital mitral stenosis (this code)Q23.3 Congenital mitral insufficiencyQ23.4 Hypoplastic left heart syndromeQ23.8 Other congenital malformations of aortic and mitral valvesQ23.81 Bicuspid aortic valveQ23.82 Congenital mitral valve cleft leaflet