Q25.42 Hypoplasia of aortaBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Defines the logic of DRG(s) 306-307 in MDC 05.
747.29 Other anomalies of aorta (approximate)I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")Q25.29 Other atresia of aortaQ25.3 Supravalvular aortic stenosisQ25.4 Other congenital malformations of aortaQ25.40 Congenital malformation of aorta unspecifiedQ25.41 Absence and aplasia of aortaQ25.42 Hypoplasia of aorta (this code)Q25.43 Congenital aneurysm of aortaQ25.44 Congenital dilation of aortaQ25.45 Double aortic archQ25.46 Tortuous aortic archQ25.47 Right aortic arch