Q25.5 Atresia of pulmonary artery

Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Risk adjustment (HCC)

• RxHCC V08: HCC 191 — Ventricular Septal Defect and Major Congenital Heart Disorders

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 747.31 Pulmonary artery coarctation and atresia (approximate)

Code annotations containing back-references to Q25.5

Back-references to Q25.5

• Type 2 Excludes: Q27 Other congenital malformations of peripheral vascular system ("anomalies of pulmonary artery (Q25.5-Q25.7)")

Back-references to Q25

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q25.5

• Atresia, atretic › artery NEC › pulmonary
• Atresia, atretic › pulmonary (artery)
• Malformation (congenital) › pulmonary › artery › atresia

Nearby codes

• Q25.45 Double aortic arch
• Q25.46 Tortuous aortic arch
• Q25.47 Right aortic arch
• Q25.48 Anomalous origin of subclavian artery
• Q25.49 Other congenital malformations of aorta
• Q25.5 Atresia of pulmonary artery (this code)
• Q25.6 Stenosis of pulmonary artery
• Q25.7 Other congenital malformations of pulmonary artery
• Q25.71 Coarctation of pulmonary artery
• Q25.72 Congenital pulmonary arteriovenous malformation
• Q25.79 Other congenital malformations of pulmonary artery