Q25.72 Congenital pulmonary arteriovenous malformation

Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital pulmonary arteriovenous aneurysm

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 747.32 Pulmonary arteriovenous malformation

Code annotations containing back-references to Q25.72

Back-references to Q25.72

• Type 1 Excludes: I28.0 Arteriovenous fistula of pulmonary vessels ("congenital arteriovenous fistula (Q25.72)")
• Type 1 Excludes: I28.1 Aneurysm of pulmonary artery ("congenital arteriovenous aneurysm (Q25.72)")

Back-references to Q25.7

• Type 2 Excludes: Q27 Other congenital malformations of peripheral vascular system ("anomalies of pulmonary artery (Q25.5-Q25.7)")

Back-references to Q25

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q25.72

• Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular) › pulmonary › arteriovenous
• Communication › between › pulmonary artery and pulmonary vein, congenital
• Fistula (cutaneous) › arteriovenous (acquired) (nonruptured) › congenital (peripheral) › pulmonary
• Fistula (cutaneous) › arteriovenous (acquired) (nonruptured) › pulmonary › congenital
• Fistula (cutaneous) › pulmonary › arteriovenous › congenital
• Malformation (congenital) › pulmonary › arteriovenous
• Shunt › arteriovenous, pulmonary (acquired) › congenital

Nearby codes

• Q25.49 Other congenital malformations of aorta
• Q25.5 Atresia of pulmonary artery
• Q25.6 Stenosis of pulmonary artery
• Q25.7 Other congenital malformations of pulmonary artery
• Q25.71 Coarctation of pulmonary artery
• Q25.72 Congenital pulmonary arteriovenous malformation (this code)
• Q25.79 Other congenital malformations of pulmonary artery
• Q25.8 Other congenital malformations of other great arteries
• Q25.9 Congenital malformation of great arteries, unspecified