Q27.0 Congenital absence and hypoplasia of umbilical artery

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Single umbilical artery

Applies from Q27 Other congenital malformations of peripheral vascular system

Excludes2 (not included here)

• anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)
• anomalies of coronary vessels (Q24.5)
• anomalies of pulmonary artery (Q25.5-Q25.7)
• congenital retinal aneurysm (Q14.1)
• hemangioma and lymphangioma (D18.-)

MS-DRG index

Defines the logic of DRG(s) 299-301 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 747.5 Absence or hypoplasia of umbilical artery

Code annotations containing back-references to Q27.0

Back-references to Q27.0

• Type 1 Excludes: P02.69 Newborn affected by other conditions of umbilical cord ("newborn affected by single umbilical artery (Q27.0)")

Back-references to Q27

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q27.0

• Absence (of) (organ or part) (complete or partial) › artery (congenital) (peripheral) › umbilical
• Absence (of) (organ or part) (complete or partial) › umbilical artery, congenital
• Agenesis › artery (peripheral) › umbilical
• Anomaly, anomalous (congenital) (unspecified type) › artery (peripheral) › umbilical
• Anomaly, anomalous (congenital) (unspecified type) › umbilical artery
• Artery, arterial › single umbilical
• Atresia, atretic › artery NEC › umbilical
• Deformity › artery (congenital) (peripheral) NOS › umbilical
• Hypoplasia, hypoplastic › artery (peripheral) › umbilical
• Hypoplasia, hypoplastic › umbilical artery
• Single › umbilical artery
• Stricture › artery › congenital (peripheral) › umbilical

Nearby codes

• Q27 Other congenital malformations of peripheral vascular system
• Q27.0 Congenital absence and hypoplasia of umbilical artery (this code)
• Q27.1 Congenital renal artery stenosis
• Q27.2 Other congenital malformations of renal artery
• Q27.3 Arteriovenous malformation (peripheral)
• Q27.30 Arteriovenous malformation, site unspecified
• Q27.31 Arteriovenous malformation of vessel of upper limb