Q27.1 Congenital renal artery stenosis

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applies from Q27 Other congenital malformations of peripheral vascular system

Excludes2 (not included here)

• anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)
• anomalies of coronary vessels (Q24.5)
• anomalies of pulmonary artery (Q25.5-Q25.7)
• congenital retinal aneurysm (Q14.1)
• hemangioma and lymphangioma (D18.-)

MS-DRG index

Defines the logic of DRG(s) 299-301 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 747.62 Renal vessel anomaly (approximate)

Code annotations containing back-references to Q27.1

Back-references to Q27.1

• Type 1 Excludes: N28.0 Ischemia and infarction of kidney ("congenital stenosis of renal artery (Q27.1)")

Back-references to Q27

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q27.1

• Stenosis, stenotic (cicatricial) › renal artery › congenital
• Stricture › renal artery › congenital

Nearby codes

• Q27 Other congenital malformations of peripheral vascular system
• Q27.0 Congenital absence and hypoplasia of umbilical artery
• Q27.1 Congenital renal artery stenosis (this code)
• Q27.2 Other congenital malformations of renal artery
• Q27.3 Arteriovenous malformation (peripheral)
• Q27.30 Arteriovenous malformation, site unspecified
• Q27.31 Arteriovenous malformation of vessel of upper limb
• Q27.32 Arteriovenous malformation of vessel of lower limb