Q87.0 Congenital malformation syndromes predominantly affecting facial appearance

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Acrocephalopolysyndactyly
• Acrocephalosyndactyly [Apert]
• Cryptophthalmos syndrome
• Cyclopia
• Goldenhar syndrome
• Moebius syndrome
• Oro-facial-digital syndrome
• Robin syndrome
• Whistling face

Applies from Q87 Other specified congenital malformation syndromes affecting multiple systems

Use additional code

• code(s) to identify all associated manifestations

MS-DRG index

Defines the logic of DRG(s) 564-566 in MDC 08.

Approximate ICD-9-CM (GEMs)

• 755.55 Acrocephalosyndactyly (approximate)
• 756.0 Anomalies of skull and face bones (approximate)

Code annotations containing back-references to Q87.0

Back-references to Q87.0

• Type 1 Excludes: M26.0 Major anomalies of jaw size ("Robin's syndrome (Q87.0)")
• Type 1 Excludes: Q04 Other congenital malformations of brain ("cyclopia (Q87.0)")
• Type 1 Excludes: Q10 Congenital malformations of eyelid, lacrimal apparatus and orbit ("cryptophthalmos syndrome (Q87.0)")
• Type 1 Excludes: Q11.2 Microphthalmos ("cryptophthalmos syndrome (Q87.0)")
• Type 1 Excludes: Q18 Other congenital malformations of face and neck ("cyclopia (Q87.0)")
• Type 1 Excludes: Q18 Other congenital malformations of face and neck ("malformation syndromes affecting facial appearance (Q87.0)")

Back-references to Q87

• Type 1 Excludes: Q67 Congenital musculoskeletal deformities of head, face, spine and chest ("congenital malformation syndromes classified to Q87.-")
• Type 1 Excludes: Q75 Other congenital malformations of skull and face bones ("congenital malformation syndromes classified to Q87.-")
• Type 1 Excludes: Q89.7 Multiple congenital malformations, not elsewhere classified ("congenital malformation syndromes affecting multiple systems (Q87.-)")

Diagnosis Index entries for Q87.0

• Acrocephalopolysyndactyly
• Acrocephalosyndactyly
• Aglossia-adactylia syndrome
• Apert's syndrome
• Carpenter's syndrome
• Cryptophthalmos › syndrome
• Cyclopia, cyclops
• Cyclopism
• Dyscranio-pygo-phalangy
• Dysplasia › oculodentodigital
• Fraser's syndrome
• Freeman Sheldon syndrome
• Goldenhar (-Gorlin) syndrome
• Gorlin-Chaudry-Moss syndrome
• Hallerman-Streiff syndrome
• Hanhart's syndrome
• Marchesani (-Weill) syndrome
• Meyer-Schwickerath and Weyers syndrome
• Moebius, Möbius › syndrome
• Moebius, Möbius › syndrome › congenital oculofacial paralysis (with other anomalies)
• Mohr's syndrome (Types I and II)
• Papillon-Léage and Psaume syndrome
• Paralysis, paralytic (complete) (incomplete) › oculofacial, congenital (Moebius)
• Pierre Robin deformity or syndrome
• Robin (-Pierre) syndrome
• Syndrome › congenital › facial diplegia
• Syndrome › congenital › oculo-auriculovertebral
• Syndrome › congenital › oculofacial diplegia (Moebius)
• Syndrome › cryptophthalmos
• Syndrome › eyelid-malar-mandible
• Syndrome › first arch
• Syndrome › micrognathia-glossoptosis
• Syndrome › oral-facial-digital
• Syndrome › oro-facial-digital
• Syndrome › oto-palatal-digital
• Syndrome › whistling face
• Tower skull › with exophthalmos
• Ullrich-Feichtiger syndrome
• Whistling face

Nearby codes

• Q87 Other specified congenital malformation syndromes affecting multiple systems
• Q87.0 Congenital malformation syndromes predominantly affecting facial appearance (this code)
• Q87.1 Congenital malformation syndromes predominantly associated with short stature
• Q87.11 Prader-Willi syndrome
• Q87.19 Other congenital malformation syndromes predominantly associated with short stature
• Q87.2 Congenital malformation syndromes predominantly involving limbs
• Q87.3 Congenital malformation syndromes involving early overgrowth