Q87.11 Prader-Willi syndrome

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applies from Q87 Other specified congenital malformation syndromes affecting multiple systems

Use additional code

• code(s) to identify all associated manifestations

Applies from Q87.1 Congenital malformation syndromes predominantly associated with short stature

Excludes1 (never code together)

• Ellis-van Creveld syndrome (Q77.6)
• Smith-Lemli-Opitz syndrome (E78.72)

Risk adjustment (HCC)

• RxHCC V08: HCC 148 — Mild or Unspecified Intellectual Disability/Developmental Disorder

MS-DRG index

Defines the logic of DRG(s) 564-566 in MDC 08.

Code annotations containing back-references to Q87.11

Back-references to Q87.11

• Type 1 Excludes: E23.3 Hypothalamic dysfunction, not elsewhere classified ("Prader-Willi syndrome (Q87.11)")
• Type 2 Excludes: E66 Overweight and obesity ("Prader-Willi syndrome (Q87.11)")

Back-references to Q87

• Type 1 Excludes: Q67 Congenital musculoskeletal deformities of head, face, spine and chest ("congenital malformation syndromes classified to Q87.-")
• Type 1 Excludes: Q75 Other congenital malformations of skull and face bones ("congenital malformation syndromes classified to Q87.-")
• Type 1 Excludes: Q89.7 Multiple congenital malformations, not elsewhere classified ("congenital malformation syndromes affecting multiple systems (Q87.-)")

Diagnosis Index entries for Q87.11

• Prader-Willi syndrome
• Syndrome › Prader-Willi

Nearby codes

• Q87 Other specified congenital malformation syndromes affecting multiple systems
• Q87.0 Congenital malformation syndromes predominantly affecting facial appearance
• Q87.1 Congenital malformation syndromes predominantly associated with short stature
• Q87.11 Prader-Willi syndrome (this code)
• Q87.19 Other congenital malformation syndromes predominantly associated with short stature
• Q87.2 Congenital malformation syndromes predominantly involving limbs
• Q87.3 Congenital malformation syndromes involving early overgrowth
• Q87.4 Marfan syndrome
• Q87.40 Marfan syndrome, unspecified