Q87.40 Marfan syndrome, unspecified

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applies from Q87 Other specified congenital malformation syndromes affecting multiple systems

Use additional code

• code(s) to identify all associated manifestations

Risk adjustment (HCC)

• RxHCC V08: HCC 84 — Systemic Lupus Erythematosus and Other Systemic Connective Tissue Disorders

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 759.82 Marfan syndrome (approximate)

Code annotations containing back-references to Q87.40

Back-references to Q87.4

• Type 1 Excludes: I34.1 Nonrheumatic mitral (valve) prolapse ("Marfan's syndrome (Q87.4-)")
• Code First: J93.12 Secondary spontaneous pneumothorax ("Marfan syndrome (Q87.4-)")

Back-references to Q87

• Type 1 Excludes: Q67 Congenital musculoskeletal deformities of head, face, spine and chest ("congenital malformation syndromes classified to Q87.-")
• Type 1 Excludes: Q75 Other congenital malformations of skull and face bones ("congenital malformation syndromes classified to Q87.-")
• Type 1 Excludes: Q89.7 Multiple congenital malformations, not elsewhere classified ("congenital malformation syndromes affecting multiple systems (Q87.-)")

Diagnosis Index entries for Q87.40

• Syndrome › Beals
• Syndrome › Marfan

Nearby codes

• Q87.11 Prader-Willi syndrome
• Q87.19 Other congenital malformation syndromes predominantly associated with short stature
• Q87.2 Congenital malformation syndromes predominantly involving limbs
• Q87.3 Congenital malformation syndromes involving early overgrowth
• Q87.4 Marfan syndrome
• Q87.40 Marfan syndrome, unspecified (this code)
• Q87.41 Marfan syndrome with cardiovascular manifestations
• Q87.410 Marfan syndrome with aortic dilation
• Q87.418 Marfan syndrome with other cardiovascular manifestations
• Q87.42 Marfan syndrome with ocular manifestations
• Q87.43 Marfan syndrome with skeletal manifestation