D64.3 Other sideroblastic anemias
Billable ICD-10-CM code, FY2026.
Applicable to
- Sideroblastic anemia NOS
- Pyridoxine-responsive sideroblastic anemia NEC
Applies from D64 Other anemias
Excludes1 (never code together)
- refractory anemia (D46.-)
- refractory anemia with excess blasts in transformation [RAEB T] (C92.0-)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 109 — Acquired Hemolytic, Aplastic, and Sideroblastic Anemias
- CMS-HCC V22: HCC 48 — Coagulation Defects and Other Specified Hematological Disorders
- RxHCC V08: HCC 96 — Acquired Hemolytic, Aplastic, and Sideroblastic Anemias
- ESRD V24: HCC 48
MS-DRG index
Defines the logic of DRG(s) 811-812 in MDC 16.
Approximate ICD-9-CM (GEMs)
285.0 Sideroblastic anemia (approximate)
Code annotations containing back-references to D64.3
Back-references to D64.3
- Type 1 Excludes:
E53.1 Pyridoxine deficiency ("pyridoxine-responsive sideroblastic anemia (D64.3)") - Type 1 Excludes:
E83.1 Disorders of iron metabolism ("sideroblastic anemia (D64.0-D64.3)")
Back-references to D64
- Code First:
M90.5 Osteonecrosis in diseases classified elsewhere ("hemoglobinopathy (D50-D64)") - Type 1 Excludes:
R71 Abnormality of red blood cells ("anemias (D50-D64)")
Diagnosis Index entries for D64.3
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › hypochromic (idiopathic) (microcytic) (normoblastic) › pyridoxine-responsive
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › pyridoxine-responsive
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › sideroblastic
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › sideroblastic › pyridoxine-responsive NEC
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › sideroblastic › specified type NEC
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › vitamin › B6-responsive
Nearby codes
D64 Other anemiasD64.0 Hereditary sideroblastic anemiaD64.1 Secondary sideroblastic anemia due to diseaseD64.2 Secondary sideroblastic anemia due to drugs and toxinsD64.3 Other sideroblastic anemias (this code)D64.4 Congenital dyserythropoietic anemiaD64.8 Other specified anemiasD64.81 Anemia due to antineoplastic chemotherapyD64.89 Other specified anemiasD64.9 Anemia, unspecified