D64.4 Congenital dyserythropoietic anemia

Billable ICD-10-CM code, FY2026.

Applicable to

• Dyshematopoietic anemia (congenital)

Excludes1 (never code together)

• Blackfan-Diamond syndrome (D61.01)
• Di Guglielmo's disease (C94.0)

Applies from D64 Other anemias

Excludes1 (never code together)

• refractory anemia (D46.-)
• refractory anemia with excess blasts in transformation [RAEB T] (C92.0-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 109 — Acquired Hemolytic, Aplastic, and Sideroblastic Anemias

MS-DRG index

Defines the logic of DRG(s) 811-812 in MDC 16.

Approximate ICD-9-CM (GEMs)

• 285.8 Other specified anemias (approximate)

Code annotations containing back-references to D64.4

Back-references to D64

• Code First: M90.5 Osteonecrosis in diseases classified elsewhere ("hemoglobinopathy (D50-D64)")
• Type 1 Excludes: R71 Abnormality of red blood cells ("anemias (D50-D64)")

Diagnosis Index entries for D64.4

• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › congenital › dyserythropoietic, dyshematopoietic
• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › dyserythropoietic (congenital)
• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › dyshematopoietic (congenital)

Nearby codes

• D64 Other anemias
• D64.0 Hereditary sideroblastic anemia
• D64.1 Secondary sideroblastic anemia due to disease
• D64.2 Secondary sideroblastic anemia due to drugs and toxins
• D64.3 Other sideroblastic anemias
• D64.4 Congenital dyserythropoietic anemia (this code)
• D64.8 Other specified anemias
• D64.81 Anemia due to antineoplastic chemotherapy
• D64.89 Other specified anemias
• D64.9 Anemia, unspecified