D68.2 Hereditary deficiency of other clotting factors
Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Applicable to
- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
Applies from D68 Other coagulation defects
Excludes1 (never code together)
- abnormal coagulation profile NOS (R79.1)
Excludes2 (not included here)
- coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
- coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 112 — Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions
- CMS-HCC V22: HCC 48 — Coagulation Defects and Other Specified Hematological Disorders
- ESRD V24: HCC 48
MS-DRG index
Defines the logic of DRG(s) 813 in MDC 16.
Approximate ICD-9-CM (GEMs)
286.3 Congenital deficiency of other clotting factors
Code annotations containing back-references to D68.2
Back-references to D68
- Type 1 Excludes:
R79.1 Abnormal coagulation profile ("coagulation defects (D68.-)")
Diagnosis Index entries for D68.2
- Absence (of) (organ or part) (complete or partial) › fibrinogen (congenital)
- Afibrinogenemia › congenital
- Defect, defective › coagulation (factor) › hereditary NEC
- Defect, defective › fibrin polymerization
- Defect, defective › Hageman (factor)
- Deficiency, deficient › accelerator globulin (Ac G) (blood)
- Deficiency, deficient › AC globulin (congenital) (hereditary)
- Deficiency, deficient › activating factor (blood)
- Deficiency, deficient › autoprothrombin › I
- Deficiency, deficient › autoprothrombin › C
- Deficiency, deficient › clotting factor NEC (hereditary)
- Deficiency, deficient › coagulation NOS › clotting factor NEC
- Deficiency, deficient › contact factor
- Deficiency, deficient › factor › Hageman
- Deficiency, deficient › factor › I (congenital) (hereditary)
- Deficiency, deficient › factor › II (congenital) (hereditary)
- Deficiency, deficient › factor › V (congenital) (hereditary)
- Deficiency, deficient › factor › VII (congenital) (hereditary)
- Deficiency, deficient › factor › X (congenital) (hereditary)
- Deficiency, deficient › factor › XII (congenital) (hereditary)
- Deficiency, deficient › factor › XIII (congenital) (hereditary)
- Deficiency, deficient › fibrin-stabilizing factor (congenital) (hereditary)
- Deficiency, deficient › fibrinase
- Deficiency, deficient › fibrinogen (congenital) (hereditary)
- Deficiency, deficient › glass factor
- Deficiency, deficient › Hageman factor
- Deficiency, deficient › labile factor (congenital) (hereditary)
- Deficiency, deficient › Laki-Lorand factor
- Deficiency, deficient › proaccelerin (congenital) (hereditary)
- Deficiency, deficient › proconvertin factor (congenital) (hereditary)
- Deficiency, deficient › prothrombin (congenital) (heredItary)
- Deficiency, deficient › Prower factor
- Deficiency, deficient › SPCA (factor VII)
- Deficiency, deficient › stable factor (congenital) (hereditary)
- Deficiency, deficient › Stuart-Prower (factor X)
- Deficiency, deficient › thrombokinase
- Disease, diseased › Hageman (congenital factor XII deficiency)
- Disease, diseased › Stuart-Prower (congenital factor X deficiency)
- Disease, diseased › Stuart's (congenital factor X deficiency)
- Dysfibrinogenemia (congenital)
- Fibrinogenopenia › congenital
- Fibrinopenia (hereditary)
- Hageman's factor defect, deficiency or disease
- Hypofibrinogenemia › congenital (hereditary)
- Hypoproconvertinemia, congenital (hereditary)
- Hypoprothrombinemia (congenital) (hereditary) (idiopathic)
- Owren's disease or syndrome (parahemophilia)
- Parahemophilia
- Stuart deficiency disease (factor X)
- Stuart-Prower factor deficiency (factor X)
Nearby codes
D68.029 Von Willebrand disease, type 2, unspecifiedD68.03 Von Willebrand disease, type 3D68.04 Acquired von Willebrand diseaseD68.09 Other von Willebrand diseaseD68.1 Hereditary factor XI deficiencyD68.2 Hereditary deficiency of other clotting factors (this code)D68.3 Hemorrhagic disorder due to circulating anticoagulantsD68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitorsD68.311 Acquired hemophiliaD68.312 Antiphospholipid antibody with hemorrhagic disorderD68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors