D68.311 Acquired hemophilia
Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Applicable to
- Autoimmune hemophilia
- Autoimmune inhibitors to clotting factors
- Secondary hemophilia
Applies from D68 Other coagulation defects
Excludes1 (never code together)
- abnormal coagulation profile NOS (R79.1)
Excludes2 (not included here)
- coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
- coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 112 — Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions
- CMS-HCC V22: HCC 48 — Coagulation Defects and Other Specified Hematological Disorders
- ESRD V24: HCC 48
MS-DRG index
Defines the logic of DRG(s) 813 in MDC 16.
Approximate ICD-9-CM (GEMs)
286.52 Acquired hemophilia
Code annotations containing back-references to D68.311
Back-references to D68
- Type 1 Excludes:
R79.1 Abnormal coagulation profile ("coagulation defects (D68.-)")
Diagnosis Index entries for D68.311
- Autoimmune › inhibitors to clotting factors
- Hemophilia (classical) (familial) (hereditary) › acquired
- Hemophilia (classical) (familial) (hereditary) › autoimmune
- Hemophilia (classical) (familial) (hereditary) › secondary
Nearby codes
D68.09 Other von Willebrand diseaseD68.1 Hereditary factor XI deficiencyD68.2 Hereditary deficiency of other clotting factorsD68.3 Hemorrhagic disorder due to circulating anticoagulantsD68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitorsD68.311 Acquired hemophilia (this code)D68.312 Antiphospholipid antibody with hemorrhagic disorderD68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitorsD68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulantsD68.4 Acquired coagulation factor deficiencyD68.5 Primary thrombophilia