D68.5 Primary thrombophilia
Non-billable header with 3 child codes.
Applicable to
- Primary hypercoagulable states
Excludes1 (never code together)
- antiphospholipid syndrome (D68.61)
- lupus anticoagulant (D68.62)
- secondary activated protein C resistance (D68.69)
- secondary antiphospholipid antibody syndrome (D68.69)
- secondary lupus anticoagulant with hypercoagulable state (D68.69)
- secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)
- systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
- systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)
- thrombotic thrombocytopenic purpura (M31.19)
Applies from D68 Other coagulation defects
Excludes1 (never code together)
- abnormal coagulation profile NOS (R79.1)
Excludes2 (not included here)
- coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
- coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Codes under D68.5
D68.51 Activated protein C resistanceD68.52 Prothrombin gene mutationD68.59 Other primary thrombophilia
Code annotations containing back-references to D68.5
Back-references to D68
- Type 1 Excludes:
R79.1 Abnormal coagulation profile ("coagulation defects (D68.-)")
Nearby codes
D68.311 Acquired hemophiliaD68.312 Antiphospholipid antibody with hemorrhagic disorderD68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitorsD68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulantsD68.4 Acquired coagulation factor deficiencyD68.5 Primary thrombophilia (this code)D68.51 Activated protein C resistanceD68.52 Prothrombin gene mutationD68.59 Other primary thrombophiliaD68.6 Other thrombophiliaD68.61 Antiphospholipid syndrome