D75.0 Familial erythrocytosis

Billable ICD-10-CM code, FY2026.

Applicable to

• Benign polycythemia
• Familial polycythemia

Excludes1 (never code together)

• hereditary ovalocytosis (D58.1)

Applies from D75 Other and unspecified diseases of blood and blood-forming organs

Excludes2 (not included here)

• acute lymphadenitis (L04.-)
• chronic lymphadenitis (I88.1)
• enlarged lymph nodes (R59.-)
• hypergammaglobulinemia NOS (D89.2)
• lymphadenitis NOS (I88.9)
• mesenteric lymphadenitis (acute) (chronic) (I88.0)

MS-DRG index

Defines the logic of DRG(s) 814-816 in MDC 16.

Approximate ICD-9-CM (GEMs)

• 289.6 Familial polycythemia

Code annotations containing back-references to D75.0

Back-references to D75.0

• Type 1 Excludes: D45 Polycythemia vera ("familial polycythemia (D75.0)")
• Type 1 Excludes: D58.2 Other hemoglobinopathies ("familial polycythemia (D75.0)")
• Type 1 Excludes: R71 Abnormality of red blood cells ("benign (familial) polycythemia (D75.0)")

Diagnosis Index entries for D75.0

• Erythrocytosis (megalosplenic) (secondary) › familial
• Polycythemia (secondary) › benign (familial)
• Polycythemia (secondary) › familial (benign)

Nearby codes

• D75 Other and unspecified diseases of blood and blood-forming organs
• D75.0 Familial erythrocytosis (this code)
• D75.1 Secondary polycythemia
• D75.8 Other specified diseases of blood and blood-forming organs
• D75.81 Myelofibrosis
• D75.82 Heparin induced thrombocytopenia (HIT)
• D75.821 Non-immune heparin-induced thrombocytopenia