E70.40 Disorders of histidine metabolism, unspecifiedBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Defines the logic of DRG(s) 642 in MDC 10.
270.5 Disturbances of histidine metabolism (approximate)E72 Other disorders of amino-acid metabolism ("aromatic amino-acid metabolism (E70.-)")G11 Hereditary ataxia ("metabolic disorders (E70-E88)")G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")R79 Other abnormal findings of blood chemistry ("specific findings indicating disorder of amino-acid metabolism (E70-E72)")R79.83 Abnormal findings of blood amino-acid level ("disorders of amino-acid metabolism (E70-E72)")E70.331 Hermansky-Pudlak syndromeE70.338 Other albinism with hematologic abnormalityE70.339 Albinism with hematologic abnormality, unspecifiedE70.39 Other specified albinismE70.4 Disorders of histidine metabolismE70.40 Disorders of histidine metabolism, unspecified (this code)E70.41 HistidinemiaE70.49 Other disorders of histidine metabolismE70.5 Disorders of tryptophan metabolismE70.8 Other disorders of aromatic amino-acid metabolismE70.81 Aromatic L-amino acid decarboxylase deficiency