E75.6 Lipid storage disorder, unspecified
Billable ICD-10-CM code, FY2026.
Applies from E75 Disorders of sphingolipid metabolism and other lipid storage disorders
Excludes1 (never code together)
- mucolipidosis, types I-III (E77.0-E77.1)
- Refsum's disease (G60.1)
Risk adjustment (HCC)
- RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
MS-DRG index
Defines the logic of DRG(s) 642 in MDC 10.
Approximate ICD-9-CM (GEMs)
272.9 Unspecified disorder of lipoid metabolism (approximate)
Code annotations containing back-references to E75.6
Back-references to E75
- Type 2 Excludes:
G11 Hereditary ataxia ("metabolic disorders (E70-E88)") - Code First:
G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)") - Type 2 Excludes:
G71 Primary disorders of muscles ("metabolic disorders (E70-E88)") - Code First:
G73.7 Myopathy in diseases classified elsewhere ("lipid storage disorders (E75.-)") - Code First:
H36 Retinal disorders in diseases classified elsewhere ("lipid storage disorders (E75.-)") - Code First:
H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)") - Type 2 Excludes:
N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88") - Type 2 Excludes:
N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88") - Type 1 Excludes:
P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)") - Type 1 Excludes:
R79 Other abnormal findings of blood chemistry ("specific findings indicating disorder of lipid metabolism (E75.-)")
Diagnosis Index entries for E75.6
- Degeneration, degenerative › brain (cortical) (progressive) › in › lipidosis › generalized
- Disease, diseased › lipid-storage
- Disorder (of) › lipid › storage
- Dystrophy, dystrophia › retinal (hereditary) › in › lipid storage disorders
- Dystrophy, dystrophia › retinal (hereditary) › in › systemic lipidoses
- Hyperlipidosis
- Lipidosis
- Myopathy › in (due to) › lipid storage disease
Nearby codes
E75.28 Canavan diseaseE75.29 Other sphingolipidosisE75.3 Sphingolipidosis, unspecifiedE75.4 Neuronal ceroid lipofuscinosisE75.5 Other lipid storage disordersE75.6 Lipid storage disorder, unspecified (this code)