`E75.5` Other lipid storage disorders

Billable ICD-10-CM code, FY2026.

Risk adjustment (HCC)

RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders

Defines the logic of DRG(s) 642 in MDC 10.

Type 1 Excludes: E78.2 Mixed hyperlipidemia ("cerebrotendinous cholesterosis [van Bogaert-Scherer- Epstein] (E75.5)")

Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
Code First: G73.7 Myopathy in diseases classified elsewhere ("lipid storage disorders (E75.-)")
Code First: H36 Retinal disorders in diseases classified elsewhere ("lipid storage disorders (E75.-)")
Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
Type 1 Excludes: R79 Other abnormal findings of blood chemistry ("specific findings indicating disorder of lipid metabolism (E75.-)")

Cholesterolosis, cholesterosis (gallbladder) › cerebrotendinous
Disease, diseased › lipid-storage › specified NEC
Disease, diseased › triglyceride-storage
Disorder (of) › lipid › storage › specified NEC
Hyperlipidosis › hereditary NEC
Lipidosis › cholesterol (cerebral)
Van Bogaert-Scherer-Epstein disease or syndrome
Wolman's disease
Xanthoma (s), xanthomatosis (primary) (familial) (hereditary) › cerebrotendinous
Xanthoma (s), xanthomatosis (primary) (familial) (hereditary) › cutaneotendinous
Xanthoma (s), xanthomatosis (primary) (familial) (hereditary) › joint
Xanthoma (s), xanthomatosis (primary) (familial) (hereditary) › tendon (sheath)