E78.89 Other lipoprotein metabolism disorders

Billable ICD-10-CM code, FY2026.

Applies from E78 Disorders of lipoprotein metabolism and other lipidemias

Excludes1 (never code together)

• sphingolipidosis (E75.0-E75.3)

Risk adjustment (HCC)

• RxHCC V08: HCC 47 — Disorders of Lipoid Metabolism

MS-DRG index

Defines the logic of DRG(s) 642 in MDC 10.

Approximate ICD-9-CM (GEMs)

• 272.8 Other disorders of lipoid metabolism (approximate)

Code annotations containing back-references to E78.89

Back-references to E78.89

• Type 1 Excludes: L98.6 Other infiltrative disorders of the skin and subcutaneous tissue ("hyalinosis cutis et mucosae (E78.89)")

Back-references to E78

• Type 2 Excludes: E88.0 Disorders of plasma-protein metabolism, not elsewhere classified ("disorder of lipoprotein metabolism (E78.-)")
• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")

Diagnosis Index entries for E78.89

• Disorder (of) › lipoprotein › metabolism › specified NEC
• Disorder (of) › metabolism NOS › lipoprotein › specified NEC
• Hyalinosis › cutis (et mucosae)
• Lipogranulomatosis
• Lipoid › proteinosis of Urbach
• Proteinosis › lipid or lipoid (of Urbach)
• Urbach's lipoid proteinosis
• Urbach-Wiethe disease

Nearby codes

• E78.71 Barth syndrome
• E78.72 Smith-Lemli-Opitz syndrome
• E78.79 Other disorders of bile acid and cholesterol metabolism
• E78.8 Other disorders of lipoprotein metabolism
• E78.81 Lipoid dermatoarthritis
• E78.89 Other lipoprotein metabolism disorders (this code)
• E78.9 Disorder of lipoprotein metabolism, unspecified