E78.9 Disorder of lipoprotein metabolism, unspecified
Billable ICD-10-CM code, FY2026.
Applies from E78 Disorders of lipoprotein metabolism and other lipidemias
Excludes1 (never code together)
- sphingolipidosis (E75.0-E75.3)
Risk adjustment (HCC)
- RxHCC V08: HCC 47 — Disorders of Lipoid Metabolism
MS-DRG index
Defines the logic of DRG(s) 642 in MDC 10.
Approximate ICD-9-CM (GEMs)
272.9 Unspecified disorder of lipoid metabolism (approximate)
Code annotations containing back-references to E78.9
Back-references to E78
- Type 2 Excludes:
E88.0 Disorders of plasma-protein metabolism, not elsewhere classified ("disorder of lipoprotein metabolism (E78.-)") - Type 2 Excludes:
G11 Hereditary ataxia ("metabolic disorders (E70-E88)") - Code First:
G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)") - Type 2 Excludes:
G71 Primary disorders of muscles ("metabolic disorders (E70-E88)") - Code First:
H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)") - Type 2 Excludes:
N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88") - Type 2 Excludes:
N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88") - Type 1 Excludes:
P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
Diagnosis Index entries for E78.9
- Disorder (of) › lipid › metabolism, congenital
- Disorder (of) › lipoprotein › metabolism
- Disorder (of) › metabolism NOS › lipoid
- Disorder (of) › metabolism NOS › lipoprotein
- Disturbance (s) › metabolism › cholesterol
- Disturbance (s) › metabolism › lipoid
- Findings, abnormal, inconclusive, without diagnosis › cholesterol
- Findings, abnormal, inconclusive, without diagnosis › triglycerides
- Lipoprotein metabolism disorder
- Osteochondrodystrophy
Nearby codes
E78.72 Smith-Lemli-Opitz syndromeE78.79 Other disorders of bile acid and cholesterol metabolismE78.8 Other disorders of lipoprotein metabolismE78.81 Lipoid dermatoarthritisE78.89 Other lipoprotein metabolism disordersE78.9 Disorder of lipoprotein metabolism, unspecified (this code)