E83.09 Other disorders of copper metabolism

Billable ICD-10-CM code, FY2026.

Applicable to

• Menkes' (kinky hair) (steely hair) disease

Applies from E83 Disorders of mineral metabolism

Excludes1 (never code together)

• dietary mineral deficiency (E58-E61)
• parathyroid disorders (E20-E21)
• vitamin D deficiency (E55.-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 50 — Amyloidosis, Porphyria, and Other Specified Metabolic Disorders
• RxHCC V08: HCC 42 — Acromegaly and Other Endocrine and Metabolic Disorders

MS-DRG index

Defines the logic of DRG(s) 642 in MDC 10.

Approximate ICD-9-CM (GEMs)

• 275.1 Disorders of copper metabolism (approximate)

Code annotations containing back-references to E83.09

Back-references to E83.09

• Type 1 Excludes: Q84.1 Congenital morphological disturbances of hair, not elsewhere classified ("Menkes' kinky hair syndrome (E83.09)")

Back-references to E83

• Type 1 Excludes: E61 Deficiency of other nutrient elements ("disorders of mineral metabolism (E83.-)")
• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
• Type 1 Excludes: R79.0 Abnormal level of blood mineral ("disorders of mineral metabolism (E83.-)")

Diagnosis Index entries for E83.09

• Disorder (of) › metabolism NOS › copper › specified type NEC
• Menkes' disease or syndrome

Nearby codes

• E83 Disorders of mineral metabolism
• E83.0 Disorders of copper metabolism
• E83.00 Disorder of copper metabolism, unspecified
• E83.01 Wilson's disease
• E83.09 Other disorders of copper metabolism (this code)
• E83.1 Disorders of iron metabolism
• E83.10 Disorder of iron metabolism, unspecified
• E83.11 Hemochromatosis
• E83.110 Hereditary hemochromatosis
• E83.111 Hemochromatosis due to repeated red blood cell transfusions