E83.110 Hereditary hemochromatosis

Billable ICD-10-CM code, FY2026.

Applicable to

• Bronzed diabetes
• Pigmentary cirrhosis (of liver)
• Primary (hereditary) hemochromatosis

Applies from E83 Disorders of mineral metabolism

Excludes1 (never code together)

• dietary mineral deficiency (E58-E61)
• parathyroid disorders (E20-E21)
• vitamin D deficiency (E55.-)

Applies from E83.1 Disorders of iron metabolism

Excludes1 (never code together)

• iron deficiency anemia (D50.-)
• sideroblastic anemia (D64.0-D64.3)

Applies from E83.11 Hemochromatosis

Excludes1 (never code together)

• GALD (P78.84)
• Gestational alloimmune liver disease (P78.84)
• Neonatal hemochromatosis (P78.84)

Risk adjustment (HCC)

• CMS-HCC V22: HCC 23 — Other Significant Endocrine and Metabolic Disorders
• RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
• ESRD V24: HCC 23

MS-DRG index

Defines the logic of DRG(s) 642 in MDC 10.

Approximate ICD-9-CM (GEMs)

• 275.01 Hereditary hemochromatosis

Code annotations containing back-references to E83.110

Back-references to E83.110

• Type 1 Excludes: K74 Fibrosis and cirrhosis of liver ("pigmentary cirrhosis (of liver) (E83.110)")
• Type 2 Excludes: K76 Other diseases of liver ("pigmentary cirrhosis (of liver) (E83.110)")

Back-references to E83.11

• Code First: M14.8 Arthropathies in other specified diseases classified elsewhere ("hemochromatosis (E83.11-)")
• Type 1 Excludes: P78.84 Gestational alloimmune liver disease ("hemochromatosis (E83.11-)")

Back-references to E83.1

• Code First: J84.03 Idiopathic pulmonary hemosiderosis ("disorders of iron metabolism (E83.1-)")

Back-references to E83

• Type 1 Excludes: E61 Deficiency of other nutrient elements ("disorders of mineral metabolism (E83.-)")
• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
• Type 1 Excludes: R79.0 Abnormal level of blood mineral ("disorders of mineral metabolism (E83.-)")

Diagnosis Index entries for E83.110

• Cirrhosis, cirrhotic (hepatic) (liver) › pigmentary
• Diabetes, diabetic (mellitus) (sugar) › bronzed
• Hemochromatosis › hereditary (primary)
• Hemochromatosis › primary

Nearby codes

• E83.01 Wilson's disease
• E83.09 Other disorders of copper metabolism
• E83.1 Disorders of iron metabolism
• E83.10 Disorder of iron metabolism, unspecified
• E83.11 Hemochromatosis
• E83.110 Hereditary hemochromatosis (this code)
• E83.111 Hemochromatosis due to repeated red blood cell transfusions
• E83.118 Other hemochromatosis
• E83.119 Hemochromatosis, unspecified
• E83.19 Other disorders of iron metabolism
• E83.2 Disorders of zinc metabolism