M30.0 Polyarteritis nodosa
Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Applies from M30 Polyarteritis nodosa and related conditions
Excludes1 (never code together)
- microscopic polyarteritis (M31.7)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 94 — Systemic Lupus Erythematosus and Other Specified Systemic Connective Tissue Disorders
- CMS-HCC V22: HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
- RxHCC V08: HCC 84 — Systemic Lupus Erythematosus and Other Systemic Connective Tissue Disorders
- ESRD V24: HCC 40
MS-DRG index
Defines the logic of DRG(s) 545-547 in MDC 08.
Approximate ICD-9-CM (GEMs)
446.0 Polyarteritis nodosa (approximate)
Code annotations containing back-references to M30.0
Back-references to M30.0
- Code Also:
D81.32 Adenosine deaminase 2 deficiency ("polyarteritis nodosa (M30.0)") - Code First:
F02 Dementia in other diseases classified elsewhere ("polyarteritis nodosa (M30.0)") - Type 1 Excludes:
L95 Vasculitis limited to skin, not elsewhere classified ("polyarteritis nodosa (M30.0)") - Type 1 Excludes:
M31.7 Microscopic polyangiitis ("polyarteritis nodosa (M30.0)")
Back-references to M30
- Type 2 Excludes:
I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)") - Type 2 Excludes:
J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)") - Code First:
J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)") - Type 1 Excludes:
L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")
Diagnosis Index entries for M30.0
- Arteritis › nodosa
- Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety) › in (due to) › polyarteritis nodosa
- Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety) › in (due to) › polyarteritis nodosa › with behavioral disturbance
- Kussmaul's › disease
- Myopathy › in (due to) › polyarteritis nodosa
- Panangiitis
- Panarteritis nodosa
- Periarteritis nodosa (disseminated) (infectious) (necrotizing)
- Polyangiitis
- Polyarteritis › nodosa
- Polyneuropathy (peripheral) › in (due to) › polyarteritis nodosa
Nearby codes
M30 Polyarteritis nodosa and related conditionsM30.0 Polyarteritis nodosa (this code)M30.1 Polyarteritis with lung involvement [Churg-Strauss]M30.2 Juvenile polyarteritisM30.3 Mucocutaneous lymph node syndrome [Kawasaki]M30.8 Other conditions related to polyarteritis nodosa