M33.00 Juvenile dermatomyositis, organ involvement unspecified

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Risk adjustment (HCC)

• CMS-HCC V28: HCC 93 — Rheumatoid Arthritis and Other Specified Inflammatory Rheumatic Disorders
• CMS-HCC V22: HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
• RxHCC V08: HCC 83 — Rheumatoid Arthritis and Other Inflammatory Polyarthropathy
• ESRD V24: HCC 40

MS-DRG index

Defines the logic of DRG(s) 545-547 in MDC 08.

Approximate ICD-9-CM (GEMs)

• 710.3 Dermatomyositis (approximate)

Code annotations containing back-references to M33.00

Back-references to M33.0

• Type 1 Excludes: M08 Juvenile arthritis ("juvenile dermatomyositis (M33.0-)")

Back-references to M33

• Type 1 Excludes: G72 Other and unspecified myopathies ("dermatopolymyositis (M33.-)")
• Type 2 Excludes: I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")
• Type 2 Excludes: J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")
• Code First: J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")
• Type 1 Excludes: L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")

Diagnosis Index entries for M33.00

• Dermatomyositis (acute) (chronic) › juvenile
• Dermatopolymyositis › juvenile

Nearby codes

• M33 Dermatopolymyositis
• M33.0 Juvenile dermatomyositis
• M33.00 Juvenile dermatomyositis, organ involvement unspecified (this code)
• M33.01 Juvenile dermatomyositis with respiratory involvement
• M33.02 Juvenile dermatomyositis with myopathy
• M33.03 Juvenile dermatomyositis without myopathy
• M33.09 Juvenile dermatomyositis with other organ involvement
• M33.1 Other dermatomyositis