M33.01 Juvenile dermatomyositis with respiratory involvement

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Risk adjustment (HCC)

• CMS-HCC V28: HCC 280 — Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders
• CMS-HCC V22: HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
• RxHCC V08: HCC 227 — Pulmonary Fibrosis, Except Idiopathic
• ESRD V24: HCC 112

MS-DRG index

Defines the logic of DRG(s) 545-547 in MDC 08.

Approximate ICD-9-CM (GEMs)

• 517.8 Lung involvement in other diseases classified elsewhere (approximate)
• 710.3 Dermatomyositis (approximate)

Code annotations containing back-references to M33.01

Back-references to M33.01

• Type 1 Excludes: J99 Respiratory disorders in diseases classified elsewhere ("dermatomyositis (M33.01, M33.11)")

Back-references to M33.0

• Type 1 Excludes: M08 Juvenile arthritis ("juvenile dermatomyositis (M33.0-)")

Back-references to M33

• Type 1 Excludes: G72 Other and unspecified myopathies ("dermatopolymyositis (M33.-)")
• Type 2 Excludes: I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")
• Type 2 Excludes: J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")
• Code First: J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")
• Type 1 Excludes: L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")

Diagnosis Index entries for M33.01

• Dermatomyositis (acute) (chronic) › juvenile › with › respiratory involvement
• Dermatopolymyositis › juvenile › with › respiratory involvement

Nearby codes

• M33 Dermatopolymyositis
• M33.0 Juvenile dermatomyositis
• M33.00 Juvenile dermatomyositis, organ involvement unspecified
• M33.01 Juvenile dermatomyositis with respiratory involvement (this code)
• M33.02 Juvenile dermatomyositis with myopathy
• M33.03 Juvenile dermatomyositis without myopathy
• M33.09 Juvenile dermatomyositis with other organ involvement
• M33.1 Other dermatomyositis
• M33.10 Other dermatomyositis, organ involvement unspecified