M33.02 Juvenile dermatomyositis with myopathyBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Defines the logic of DRG(s) 545-547 in MDC 08.
359.6 Symptomatic inflammatory myopathy in diseases classified elsewhere (approximate)710.3 Dermatomyositis (approximate)M08 Juvenile arthritis ("juvenile dermatomyositis (M33.0-)")G72 Other and unspecified myopathies ("dermatopolymyositis (M33.-)")I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)")J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)")J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)")L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")M33 DermatopolymyositisM33.0 Juvenile dermatomyositisM33.00 Juvenile dermatomyositis, organ involvement unspecifiedM33.01 Juvenile dermatomyositis with respiratory involvementM33.02 Juvenile dermatomyositis with myopathy (this code)M33.03 Juvenile dermatomyositis without myopathyM33.09 Juvenile dermatomyositis with other organ involvementM33.1 Other dermatomyositisM33.10 Other dermatomyositis, organ involvement unspecifiedM33.11 Other dermatomyositis with respiratory involvement