Q22.1 Congenital pulmonary valve stenosis

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 746.02 Stenosis of pulmonary valve, congenital

Code annotations containing back-references to Q22.1

Back-references to Q22.1

• Type 1 Excludes: I37 Nonrheumatic pulmonary valve disorders ("pulmonary valve disorder specified as congenital (Q22.1, Q22.2, Q22.3)")

Back-references to Q22

• Type 2 Excludes: I08 Multiple valve diseases ("multiple valve disease specified as nonrheumatic (I34.-, I35.-, I36.-, I37.-, I38.-, Q22.-, Q23.-, Q24.8-)")
• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q22.1

• Anomaly, anomalous (congenital) (unspecified type) › heart › valve NEC › pulmonary › stenosis
• Anomaly, anomalous (congenital) (unspecified type) › pulmonary › valve › stenosis
• Fusion, fused (congenital) › cusps, heart valve NEC › pulmonary
• Fusion, fused (congenital) › pulmonic cusps
• Stenosis, stenotic (cicatricial) › pulmonary (artery) (congenital) › valve › congenital
• Stenosis, stenotic (cicatricial) › pulmonic (congenital)
• Stenosis, stenotic (cicatricial) › valve (cardiac) (heart) › congenital › pulmonary
• Stricture › heart › valve › pulmonary
• Stricture › pulmonary, pulmonic › valve › congenital
• Stricture › valve (cardiac) (heart) › congenital › pulmonary

Nearby codes

• Q22 Congenital malformations of pulmonary and tricuspid valves
• Q22.0 Pulmonary valve atresia
• Q22.1 Congenital pulmonary valve stenosis (this code)
• Q22.2 Congenital pulmonary valve insufficiency
• Q22.3 Other congenital malformations of pulmonary valve
• Q22.4 Congenital tricuspid stenosis
• Q22.5 Ebstein's anomaly
• Q22.6 Hypoplastic right heart syndrome