Q22.3 Other congenital malformations of pulmonary valve

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital malformation of pulmonary valve NOS
• Supernumerary cusps of pulmonary valve

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 746.00 Congenital pulmonary valve anomaly, unspecified (approximate)

Code annotations containing back-references to Q22.3

Back-references to Q22.3

• Type 1 Excludes: I37 Nonrheumatic pulmonary valve disorders ("pulmonary valve disorder specified as congenital (Q22.1, Q22.2, Q22.3)")

Back-references to Q22

• Type 2 Excludes: I08 Multiple valve diseases ("multiple valve disease specified as nonrheumatic (I34.-, I35.-, I36.-, I37.-, I38.-, Q22.-, Q23.-, Q24.8-)")
• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q22.3

• Accessory (congenital) › cusp (s), heart valve NEC › pulmonary
• Accessory (congenital) › heart › valve NEC › pulmonary
• Accessory (congenital) › valve, heart NEC › pulmonary
• Anomaly, anomalous (congenital) (unspecified type) › cardiac › valve NEC › pulmonary
• Anomaly, anomalous (congenital) (unspecified type) › heart › valve NEC › pulmonary
• Anomaly, anomalous (congenital) (unspecified type) › pulmonary › valve
• Anomaly, anomalous (congenital) (unspecified type) › pulmonary › valve › specified type NEC
• Anomaly, anomalous (congenital) (unspecified type) › valve (heart) NEC › pulmonary
• Development › defective, congenital › valve › pulmonary
• Dilatation › cardiac (acute) (chronic) › congenital › valve NEC › pulmonary
• Dilatation › pulmonary › valve, congenital
• Disease, diseased › heart (organic) › valve, valvular (obstructive) (regurgitant) › congenital NEC › pulmonary
• Fallot's › triad or trilogy
• Fenestration, fenestrated › cusps, heart valve NEC › pulmonary
• Fenestration, fenestrated › pulmonic cusps
• Imperfect › closure (congenital) › cusps, heart valve NEC › pulmonary
• Incompetency, incompetent, incompetence › pulmonary valve (heart) › congenital
• Malformation (congenital) › pulmonary › valve
• Supernumerary (congenital) › cusps, heart valve NEC › pulmonary
• Supernumerary (congenital) › pulmonary, pulmonic cusps

Nearby codes

• Q22 Congenital malformations of pulmonary and tricuspid valves
• Q22.0 Pulmonary valve atresia
• Q22.1 Congenital pulmonary valve stenosis
• Q22.2 Congenital pulmonary valve insufficiency
• Q22.3 Other congenital malformations of pulmonary valve (this code)
• Q22.4 Congenital tricuspid stenosis
• Q22.5 Ebstein's anomaly
• Q22.6 Hypoplastic right heart syndrome
• Q22.8 Other congenital malformations of tricuspid valve
• Q22.9 Congenital malformation of tricuspid valve, unspecified