Q22.4 Congenital tricuspid stenosisBillable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.
Defines the logic of DRG(s) 306-307 in MDC 05.
746.1 Tricuspid atresia and stenosis, congenital (approximate)I36 Nonrheumatic tricuspid valve disorders ("tricuspid valve disorders specified as congenital (Q22.4, Q22.8, Q22.9)")I08 Multiple valve diseases ("multiple valve disease specified as nonrheumatic (I34.-, I35.-, I36.-, I37.-, I38.-, Q22.-, Q23.-, Q24.8-)")I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")Q22 Congenital malformations of pulmonary and tricuspid valvesQ22.0 Pulmonary valve atresiaQ22.1 Congenital pulmonary valve stenosisQ22.2 Congenital pulmonary valve insufficiencyQ22.3 Other congenital malformations of pulmonary valveQ22.4 Congenital tricuspid stenosis (this code)Q22.5 Ebstein's anomalyQ22.6 Hypoplastic right heart syndromeQ22.8 Other congenital malformations of tricuspid valveQ22.9 Congenital malformation of tricuspid valve, unspecified