Q89.01 Asplenia (congenital)

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applies from Q89.0 Congenital absence and malformations of spleen

Excludes1 (never code together)

• isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)

MS-DRG index

Defines the logic of DRG(s) 814-816 in MDC 16.

Approximate ICD-9-CM (GEMs)

• 759.0 Anomalies of spleen (approximate)

Code annotations containing back-references to Q89.01

Back-references to Q89.01

• Type 1 Excludes: D73.0 Hyposplenism ("asplenia (congenital) (Q89.01)")

Back-references to Q89.0

• Type 1 Excludes: D73.1 Hypersplenism ("splenomegaly congenital (Q89.0)")

Diagnosis Index entries for Q89.01

• Absence (of) (organ or part) (complete or partial) › spleen (congenital)
• Agenesis › spleen
• Anomaly, anomalous (congenital) (unspecified type) › spleen › agenesis
• Aplasia › spleen
• Asplenia (congenital)
• Ivemark's syndrome (asplenia with congenital heart disease)
• Syndrome › Ivemark's
• Syndrome › splenic › agenesis

Nearby codes

• Q89 Other congenital malformations, not elsewhere classified
• Q89.0 Congenital absence and malformations of spleen
• Q89.01 Asplenia (congenital) (this code)
• Q89.09 Congenital malformations of spleen
• Q89.1 Congenital malformations of adrenal gland
• Q89.2 Congenital malformations of other endocrine glands
• Q89.3 Situs inversus
• Q89.4 Conjoined twins