Q89.09 Congenital malformations of spleen

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital splenomegaly

Applies from Q89.0 Congenital absence and malformations of spleen

Excludes1 (never code together)

• isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)

MS-DRG index

Defines the logic of DRG(s) 814-816 in MDC 16.

Approximate ICD-9-CM (GEMs)

• 759.0 Anomalies of spleen (approximate)

Code annotations containing back-references to Q89.09

Back-references to Q89.0

• Type 1 Excludes: D73.1 Hypersplenism ("splenomegaly congenital (Q89.0)")

Diagnosis Index entries for Q89.09

• Aberrant (congenital) › spleen
• Accessory (congenital) › spleen
• Anomaly, anomalous (congenital) (unspecified type) › spleen
• Cyst (colloid) (mucous) (simple) (retention) › spleen NEC › congenital
• Deformity › spleen › congenital
• Disease, diseased › polycystic › spleen
• Disease, diseased › spleen › polycystic
• Displacement, displaced › spleen (congenital)
• Distortion (s) (congenital) › spleen
• Ectopic, ectopia (congenital) › spleen
• Lobulation (congenital) › spleen
• Malformation (congenital) › spleen
• Malposition › congenital › spleen
• Polycystic (disease) › spleen
• Polysplenia syndrome
• Splenomegaly, splenomegalia (Bengal) (cryptogenic) (idiopathic) (tropical) › congenital
• Supernumerary (congenital) › spleen
• Syndrome › polysplenia

Nearby codes

• Q89 Other congenital malformations, not elsewhere classified
• Q89.0 Congenital absence and malformations of spleen
• Q89.01 Asplenia (congenital)
• Q89.09 Congenital malformations of spleen (this code)
• Q89.1 Congenital malformations of adrenal gland
• Q89.2 Congenital malformations of other endocrine glands
• Q89.3 Situs inversus
• Q89.4 Conjoined twins
• Q89.7 Multiple congenital malformations, not elsewhere classified