C88.2 Heavy chain disease

Non-billable header with 2 child codes.

Applicable to

• Franklin disease
• Gamma heavy chain disease
• Mu heavy chain disease

Applies from C88 Malignant immunoproliferative diseases and certain other B-cell lymphomas

Excludes1 (never code together)

• B-cell lymphoma, unspecified (C85.1-)
• personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79)

Codes under C88.2

• C88.20 Heavy chain disease not having achieved remission
• C88.21 Heavy chain disease, in remission

Approximate ICD-9-CM (GEMs)

• 203.80 Other immunoproliferative neoplasms, without mention of having achieved remission (approximate)
• 203.81 Other immunoproliferative neoplasms, in remission (approximate)

Code annotations containing back-references to C88.2

Back-references to C88

• Type 1 Excludes: C76 Malignant neoplasm of other and ill-defined sites ("malignant neoplasm of lymphoid, hematopoietic and related tissue (C81-C96)")
• Type 1 Excludes: C77 Secondary and unspecified malignant neoplasm of lymph nodes ("malignant neoplasm of lymph nodes, specified as primary (C81-C86, C88, C96.-)")
• Code First: Z15.0 Genetic susceptibility to malignant neoplasm (", if applicable, any current malignant neoplasm (C00-C75, C81-C96)")

Diagnosis Index entries for C88.2

• Disease, diseased › Franklin
• Disease, diseased › gamma heavy chain
• Disease, diseased › heavy chain NEC
• Disease, diseased › heavy chain NEC › gamma
• Disease, diseased › heavy chain NEC › mu
• Disease, diseased › mu heavy chain disease
• Franklin disease

Nearby codes

• C88 Malignant immunoproliferative diseases and certain other B-cell lymphomas
• C88.0 Waldenstrom macroglobulinemia
• C88.00 Waldenstrom macroglobulinemia not having achieved remission
• C88.01 Waldenstrom macroglobulinemia, in remission
• C88.2 Heavy chain disease (this code)
• C88.20 Heavy chain disease not having achieved remission
• C88.21 Heavy chain disease, in remission
• C88.3 Immunoproliferative small intestinal disease
• C88.30 Immunoproliferative small intestinal disease not having achieved remission
• C88.31 Immunoproliferative small intestinal disease, in remission