C88.3 Immunoproliferative small intestinal disease

Non-billable header with 2 child codes.

Applicable to

• Alpha heavy chain disease
• Mediterranean lymphoma

Applies from C88 Malignant immunoproliferative diseases and certain other B-cell lymphomas

Excludes1 (never code together)

• B-cell lymphoma, unspecified (C85.1-)
• personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79)

Codes under C88.3

• C88.30 Immunoproliferative small intestinal disease not having achieved remission
• C88.31 Immunoproliferative small intestinal disease, in remission

Approximate ICD-9-CM (GEMs)

• 203.80 Other immunoproliferative neoplasms, without mention of having achieved remission (approximate)

Code annotations containing back-references to C88.3

Back-references to C88

• Type 1 Excludes: C76 Malignant neoplasm of other and ill-defined sites ("malignant neoplasm of lymphoid, hematopoietic and related tissue (C81-C96)")
• Type 1 Excludes: C77 Secondary and unspecified malignant neoplasm of lymph nodes ("malignant neoplasm of lymph nodes, specified as primary (C81-C86, C88, C96.-)")
• Code First: Z15.0 Genetic susceptibility to malignant neoplasm (", if applicable, any current malignant neoplasm (C00-C75, C81-C96)")

Diagnosis Index entries for C88.3

• Disease, diseased › alpha heavy chain
• Disease, diseased › heavy chain NEC › alpha
• Disease, diseased › immunoproliferative (malignant) › small intestinal
• Lymphoma (of) (malignant) › Mediterranean

Nearby codes

• C88.00 Waldenstrom macroglobulinemia not having achieved remission
• C88.01 Waldenstrom macroglobulinemia, in remission
• C88.2 Heavy chain disease
• C88.20 Heavy chain disease not having achieved remission
• C88.21 Heavy chain disease, in remission
• C88.3 Immunoproliferative small intestinal disease (this code)
• C88.30 Immunoproliferative small intestinal disease not having achieved remission
• C88.31 Immunoproliferative small intestinal disease, in remission
• C88.4 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]
• C88.40 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission
• C88.41 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma], in remission