D61.02 Shwachman-Diamond syndrome

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Use additional code

• code, if applicable, for genetic susceptibility to other malignant neoplasm (Z15.09)

Code also

• , if applicable, associated conditions such as:
• acute myeloblastic leukemia (C92.0-)
• exocrine pancreatic insufficiency (K86.81)
• myelodysplastic syndrome (D46.-)

Applies from D61 Other aplastic anemias and other bone marrow failure syndromes

Excludes2 (not included here)

• neutropenia (D70.-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 109 — Acquired Hemolytic, Aplastic, and Sideroblastic Anemias
• CMS-HCC V22: HCC 46 — Severe Hematological Disorders
• RxHCC V08: HCC 96 — Acquired Hemolytic, Aplastic, and Sideroblastic Anemias
• ESRD V24: HCC 46

MS-DRG index

Defines the logic of DRG(s) 808-810 in MDC 16.

Code annotations containing back-references to D61.02

Back-references to D61

• Code First: M90.5 Osteonecrosis in diseases classified elsewhere ("hemoglobinopathy (D50-D64)")
• Type 1 Excludes: R71 Abnormality of red blood cells ("anemias (D50-D64)")

Diagnosis Index entries for D61.02

• Syndrome › Schwachman (-Diamond)
• Syndrome › Shwachman (-Diamond)

Nearby codes

• D61 Other aplastic anemias and other bone marrow failure syndromes
• D61.0 Constitutional aplastic anemia
• D61.01 Constitutional (pure) red blood cell aplasia
• D61.02 Shwachman-Diamond syndrome (this code)
• D61.03 Fanconi anemia
• D61.09 Other constitutional aplastic anemia
• D61.1 Drug-induced aplastic anemia
• D61.2 Aplastic anemia due to other external agents
• D61.3 Idiopathic aplastic anemia