D61.09 Other constitutional aplastic anemia
Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Applicable to
- Pancytopenia with malformations
Applies from D61 Other aplastic anemias and other bone marrow failure syndromes
Excludes2 (not included here)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 109 — Acquired Hemolytic, Aplastic, and Sideroblastic Anemias
- CMS-HCC V22: HCC 46 — Severe Hematological Disorders
- RxHCC V08: HCC 96 — Acquired Hemolytic, Aplastic, and Sideroblastic Anemias
- ESRD V24: HCC 46
MS-DRG index
Defines the logic of DRG(s) 808-810 in MDC 16.
Approximate ICD-9-CM (GEMs)
284.09 Other constitutional aplastic anemia
Code annotations containing back-references to D61.09
Back-references to D61.09
- Type 1 Excludes:
E79 Disorders of purine and pyrimidine metabolism ("Fanconi's anemia (D61.09)")
Back-references to D61
- Code First:
M90.5 Osteonecrosis in diseases classified elsewhere ("hemoglobinopathy (D50-D64)") - Type 1 Excludes:
R71 Abnormality of red blood cells ("anemias (D50-D64)")
Diagnosis Index entries for D61.09
- Aleukia › hemorrhagica › congenital
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › aplastic › congenital
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › aregenerative › congenital
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › chronica congenita aregenerativa
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › congenital › aplastic
- Erythroblastophthisis
- Erythrogenesis imperfecta
- Pancytopenia (acquired) › with › malformations
- Pancytopenia (acquired) › congenital
- Panhematopenia › congenital
- Panhematopenia › constitutional
- Panhemocytopenia › congenital
- Panhemocytopenia › constitutional
- Panmyelopathy, familial, constitutional
- Panmyelophthisis › congenital
Nearby codes
D61 Other aplastic anemias and other bone marrow failure syndromesD61.0 Constitutional aplastic anemiaD61.01 Constitutional (pure) red blood cell aplasiaD61.02 Shwachman-Diamond syndromeD61.03 Fanconi anemiaD61.09 Other constitutional aplastic anemia (this code)D61.1 Drug-induced aplastic anemiaD61.2 Aplastic anemia due to other external agentsD61.3 Idiopathic aplastic anemiaD61.8 Other specified aplastic anemias and other bone marrow failure syndromesD61.81 Pancytopenia