E76.219 Morquio mucopolysaccharidoses, unspecified

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Morquio syndrome
• Mucopolysaccharidosis, type IV

Risk adjustment (HCC)

• CMS-HCC V28: HCC 49 — Specified Lysosomal Storage Disorders
• CMS-HCC V22: HCC 23 — Other Significant Endocrine and Metabolic Disorders
• RxHCC V08: HCC 41 — Lysosomal Storage Disorders
• ESRD V24: HCC 23

MS-DRG index

Defines the logic of DRG(s) 642 in MDC 10.

Approximate ICD-9-CM (GEMs)

• 277.5 Mucopolysaccharidosis (approximate)

Code annotations containing back-references to E76.219

Back-references to E76.2

• Type 1 Excludes: E74 Other disorders of carbohydrate metabolism ("mucopolysaccharidosis (E76.0-E76.3)")
• Type 1 Excludes: Q77 Osteochondrodysplasia with defects of growth of tubular bones and spine ("mucopolysaccharidosis (E76.0-E76.3)")

Back-references to E76

• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")

Diagnosis Index entries for E76.219

• Chondro-osteodysplasia (Morquio-Brailsford type)
• Kyphosis, kyphotic (acquired) › Morquio-Brailsford type (spinal)
• Mucopolysaccharidosis › Morquio syndrome
• Mucopolysaccharidosis › type › IV

Nearby codes

• E76.1 Mucopolysaccharidosis, type II
• E76.2 Other mucopolysaccharidoses
• E76.21 Morquio mucopolysaccharidoses
• E76.210 Morquio A mucopolysaccharidoses
• E76.211 Morquio B mucopolysaccharidoses
• E76.219 Morquio mucopolysaccharidoses, unspecified (this code)
• E76.22 Sanfilippo mucopolysaccharidoses
• E76.29 Other mucopolysaccharidoses
• E76.3 Mucopolysaccharidosis, unspecified
• E76.8 Other disorders of glucosaminoglycan metabolism
• E76.9 Glucosaminoglycan metabolism disorder, unspecified