E76.9 Glucosaminoglycan metabolism disorder, unspecified
Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Risk adjustment (HCC)
- CMS-HCC V22: HCC 23 — Other Significant Endocrine and Metabolic Disorders
- RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
- ESRD V24: HCC 23
MS-DRG index
Defines the logic of DRG(s) 642 in MDC 10.
Approximate ICD-9-CM (GEMs)
277.5 Mucopolysaccharidosis (approximate)
Code annotations containing back-references to E76.9
Back-references to E76
- Type 2 Excludes:
G11 Hereditary ataxia ("metabolic disorders (E70-E88)") - Code First:
G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)") - Type 2 Excludes:
G71 Primary disorders of muscles ("metabolic disorders (E70-E88)") - Code First:
H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)") - Type 2 Excludes:
N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88") - Type 2 Excludes:
N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88") - Type 1 Excludes:
P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")
Diagnosis Index entries for E76.9
- Disorder (of) › metabolism NOS › glucosaminoglycan
- Disorder (of) › metabolism NOS › glycosaminoglycan
Nearby codes
E76.219 Morquio mucopolysaccharidoses, unspecifiedE76.22 Sanfilippo mucopolysaccharidosesE76.29 Other mucopolysaccharidosesE76.3 Mucopolysaccharidosis, unspecifiedE76.8 Other disorders of glucosaminoglycan metabolismE76.9 Glucosaminoglycan metabolism disorder, unspecified (this code)