E76.8 Other disorders of glucosaminoglycan metabolismBillable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.
Defines the logic of DRG(s) 642 in MDC 10.
277.5 Mucopolysaccharidosis (approximate)G11 Hereditary ataxia ("metabolic disorders (E70-E88)")G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")E76.211 Morquio B mucopolysaccharidosesE76.219 Morquio mucopolysaccharidoses, unspecifiedE76.22 Sanfilippo mucopolysaccharidosesE76.29 Other mucopolysaccharidosesE76.3 Mucopolysaccharidosis, unspecifiedE76.8 Other disorders of glucosaminoglycan metabolism (this code)E76.9 Glucosaminoglycan metabolism disorder, unspecified