E88.11 Partial lipodystrophy

Billable ICD-10-CM code, FY2026.

Applicable to

• Acquired partial lipodystrophy (APL)
• Barraquer-Simons lipodystrophy
• Familial partial lipodystrophy (FPLD)

Applies from E88 Other and unspecified metabolic disorders

Excludes1 (never code together)

• histiocytosis X (chronic) (C96.6)

Use additional code

• codes for associated conditions

Applies from E88.1 Lipodystrophy, not elsewhere classified

Excludes1 (never code together)

• Whipple's disease (K90.81)

MS-DRG index

Defines the logic of DRG(s) 642 in MDC 10.

Code annotations containing back-references to E88.11

Back-references to E88

• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")

Diagnosis Index entries for E88.11

• APL (acquired partial lipodystrophy)
• Barraquer (-Simons) disease or syndrome (progressive lipodystrophy)
• Disease, diseased › Barraquer (-Simons') (progressive lipodystrophy)
• Disease, diseased › Simons' (progressive lipodystrophy)
• Lipodystrophia progressiva
• Lipodystrophy › partial (acquired) (familial)
• Lipodystrophy › progressive
• Simons' disease or syndrome (progressive lipodystrophy)
• Syndrome › Simons'

Nearby codes

• E88.01 Alpha-1-antitrypsin deficiency
• E88.02 Plasminogen deficiency
• E88.09 Other disorders of plasma-protein metabolism, not elsewhere classified
• E88.1 Lipodystrophy, not elsewhere classified
• E88.10 Lipodystrophy, unspecified
• E88.11 Partial lipodystrophy (this code)
• E88.12 Generalized lipodystrophy
• E88.13 Localized lipodystrophy
• E88.14 HIV-associated lipodystrophy
• E88.19 Other lipodystrophy, not elsewhere classified
• E88.2 Lipomatosis, not elsewhere classified