E88.89 Other specified metabolic disorders

Billable ICD-10-CM code, FY2026.

Applicable to

• Launois-Bensaude adenolipomatosis

Excludes1 (never code together)

• adult pulmonary Langerhans cell histiocytosis (J84.82)

Applies from E88 Other and unspecified metabolic disorders

Excludes1 (never code together)

• histiocytosis X (chronic) (C96.6)

Use additional code

• codes for associated conditions

Risk adjustment (HCC)

• CMS-HCC V28: HCC 50 — Amyloidosis, Porphyria, and Other Specified Metabolic Disorders
• CMS-HCC V22: HCC 23 — Other Significant Endocrine and Metabolic Disorders
• RxHCC V08: HCC 43 — Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
• ESRD V24: HCC 23

MS-DRG index

Defines the logic of DRG(s) 642 in MDC 10.

Approximate ICD-9-CM (GEMs)

• 272.8 Other disorders of lipoid metabolism (approximate)
• 277.89 Other specified disorders of metabolism (approximate)

Code annotations containing back-references to E88.89

Back-references to E88

• Type 2 Excludes: G11 Hereditary ataxia ("metabolic disorders (E70-E88)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("metabolic diseases (E70-E88)")
• Type 2 Excludes: G71 Primary disorders of muscles ("metabolic disorders (E70-E88)")
• Code First: H42 Glaucoma in diseases classified elsewhere ("specified metabolic disorder (E70-E88)")
• Type 2 Excludes: N25.0 Renal osteodystrophy ("metabolic disorders classifiable to E70-E88")
• Type 2 Excludes: N25.81 Secondary hyperparathyroidism of renal origin ("metabolic disorders classifiable to E70-E88")
• Type 1 Excludes: P59 Neonatal jaundice from other and unspecified causes ("jaundice due to inborn errors of metabolism (E70-E88)")

Diagnosis Index entries for E88.89

• Adenolipomatosis, Launois-Bensaude
• Deficiency, deficient › dihydropyrimidine dehydrogenase (DPD)
• Dihydropyrimidine dehydrogenase disease (DPD)
• Disease, diseased › Erdheim-Chester (ECD)
• Disorder (of) › metabolism NOS › specified NEC
• DPD (dihydropyrimidine dehydrogenase deficiency)
• Hoffa-Kastert disease
• Hoffa's disease
• Ketosis NEC
• Launois-Bensaude adenolipomatosis
• Lipomatosis › Launois-Bensaude
• Liposynovitis prepatellaris
• Madelung's › disease › symmetrical lipomas, neck
• Steatosis
• Syndrome › Erdheim-Chester (ECD)

Nearby codes

• E88.810 Metabolic syndrome
• E88.811 Insulin resistance syndrome, Type A
• E88.818 Other insulin resistance
• E88.819 Insulin resistance, unspecified
• E88.82 Obesity due to disruption of MC4R pathway
• E88.89 Other specified metabolic disorders (this code)
• E88.9 Metabolic disorder, unspecified
• E88.A Wasting disease (syndrome) due to underlying condition